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. 2017 Mar 13;28(8):2472–2481. doi: 10.1681/ASN.2016060637

Table 1.

Description of patients included in this study

Patient No. Sex Age at Sampling Diagnosis ANCA Clinical Findings Creatinine,a μmol/L BP at Admission, mmHg BVAS Score Blood Sample Taken Before/After Start of Immunosuppressive Therapy
1 M 43 HSP — Purpura, nephritis, arthritis 89 170/100 15 B
2 M 16 HSP — Purpura, arthritis 69 122/70 3 B
3b M 80 MPA MPO Rash, nephritis 259 168/72 23 B
4 M 62 GPA PR3 URT symptoms, pulmonary granuloma, temporal arteritis 61 130/90 6 B
5b F 19 SLE — Rash, myalgia, scleritis, nephritis 62 110/60 17 A
6b F 76 GPA PR3 Gingivitis, rhinitis, hematuria 74 130/70 14 B
7b F 12 GPA PR3 MPO Fever, arthralgia, nephritis 312 120/70 15 A
8b F 61 GPA MPO Polychondritis, cough, rhinitis, nephritis 54 150/80 13 B
9 M 10 HSP — Purpura, arthritis, nephritis 47 102/60 7 B
10 F 51 GPA PR3 Hemoptysis, cough, nephritis 132 164/96 8 A
11 M 73 MPA MPO Hearing loss, nephritis 173 155/93 15 A
12 F 68 GPA PR3 Myalgia, arthralgia, nephritis 86 136/79 13 A
13 F 67 MPA MPO Myalgia, confusion, nephritis 148 130/60 22 B
14 F 9 HSP — Purpura, myalgia, nephritis, arthritis 51 110/62 18 B
15 M 13 GPA PR3 Dyspnea, pulmonary infiltrates, arthralgia, nephritis 84 120/70 24 B
16 F 17 GPA MPO Dyspnea, myalgia, arthralgia, gastrointestinal symptoms, nephritis 86 115/75 26 B
17 F 13 GPA PR3 Myalgia, pansinusitis, exophthalmos, pulmonary infiltrates 48 110/75 17 B

M, male; —, no ANCA detected; B, before; MPA, microscopic polyangiitis; MPO, myeloperoxidase; GPA, granulomatosis with polyangiitis; URT, upper respiratory tract; F, female; A, after.

a

Normal creatinine values of 45–90 μmol/L for women and 60–105 μmol/L for men.

b

These patients were previously described, including their kinin levels.2,23