Table 1.
SGC densities measurements in cochlea from 6-month-old +/Pcdh15av-3J single heterozygotes controls, Cdh23v-2J +/+ Pcdh15av-3J double heterozygotes and Pcdh15av-3J/Pcdh15av-3J single homozygotes
| Cochlear turn | +/Pcdh15av-3J | Cdh23v-2J +/+ Pcdh15av-3J | Pcdh15av-3J/Pcdh15av-3J |
|---|---|---|---|
| Mid-apex | 39.2 ± 1.5 | 38.4 ± 1.1 | 13 ± 0.7* |
| Mid-base | 34 ± 1.6 | 24.2 ± 1.3* | 8.4 ± 1.1* |
| Basal hook | 20.2 ± 1.3 | 5.2 ± 1.9* | 3.6 ± 1.1* |
SGC measurements (cells per 10 000 μm2) were obtained from four cochleae from each genotype.
Significantly different (P < 0.001) compared with +/Pcdh15av-3J.